Henoch-Schonlein purpura

Background

  • Usually affects 2-11yr
  • 5% of cases are a/w intussusception (abd vasculitis)
  • Renal involvement is feared complication
  • 95% recover completely

Diagnosis

  • Triad:
    • Purpuric rash (lower extremity, buttock)
    • Acute abdominal pain (Diffuse, colicky)
      • Develops after onset of rash
    • Arthritis
      • Migratory, usually involves knees/ankles

DDx

  1. Meningococcemia
  2. Erythema nodosum
  3. Intussusception
  4. Rheumatic fever
  5. Polyarteritis nodosa
  6. SLE
  7. RA
  8. Drug reaction

Work-Up

  1. UA
    1. If +hematuria obtain chemistry

Treatment

  • Supportive
  • NSAIDs for pain

Disposition

  • Outpt management for most w/ rheum f/u

Source

Rosen's, Tintinalli