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==Background==
==Background==
*Most common vasculitis in childhood
*Usually affects 2-11yr
*Usually affects 2-11yr
*5% of cases are a/w intussusception (abd vasculitis)
*5% of cases are a/w intussusception (abd vasculitis)
*Renal involvement is feared complication
*Renal involvement is feared complication
*95% recover completely
*95% recover completely after 3-4wk


==Diagnosis==
==Diagnosis==
*Triad:
*Tetrad:
**Purpuric rash (lower extremity, buttock)
**Palpable purpura (extremities, buttock)
**Acute abdominal pain (Diffuse, colicky)
**Acute abdominal pain (diffuse, colicky)
***Develops after onset of rash
***Develops after onset of rash
**Arthritis
**Arthritis
***Migratory, usually involves knees/ankles
***Migratory, usually involves knees/ankles
**Renal disease (50%)


==DDx==
==DDx==

Revisión del 18:25 28 jun 2011

Background

  • Most common vasculitis in childhood
  • Usually affects 2-11yr
  • 5% of cases are a/w intussusception (abd vasculitis)
  • Renal involvement is feared complication
  • 95% recover completely after 3-4wk

Diagnosis

  • Tetrad:
    • Palpable purpura (extremities, buttock)
    • Acute abdominal pain (diffuse, colicky)
      • Develops after onset of rash
    • Arthritis
      • Migratory, usually involves knees/ankles
    • Renal disease (50%)

DDx

  1. Meningococcemia
  2. Erythema nodosum
  3. Intussusception
  4. Rheumatic fever
  5. Polyarteritis nodosa
  6. SLE
  7. RA
  8. Drug reaction

Work-Up

  1. UA
    1. Hematuria, proteinuria
  2. Chemistry

Treatment

  • Supportive
  • NSAIDs for pain

Disposition

  • Outpt management for most w/ rheum f/u

Source

Rosen's, Tintinalli