Diferencia entre revisiones de «Henoch-Schonlein purpura»

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==Background==
==Background==
-HSP, aka anaphylactoid purpura
-HSP, aka anaphylactoid purpura


Línea 9: Línea 7:


-commonly occurs in springtime after viral URI
-commonly occurs in springtime after viral URI


==Diagnosis==
==Diagnosis==
-clinical diagnosis based on presence of abdominal pain, classic rash, microscopic hematuria, arthralgias in otherwise well appearing child
-clinical diagnosis based on presence of abdominal pain, classic rash, microscopic hematuria, arthralgias in otherwise well appearing child


Línea 22: Línea 16:


-intussusception: ileoileal more common than ileocolic inpatients with HSP
-intussusception: ileoileal more common than ileocolic inpatients with HSP


==Work-Up==
==Work-Up==
 
#CBC, Chem7
 
#UA
-CBC, Chem7
#Blood cx
 
#ESR
-UA
#consider CT abdomen (ileoileal intussusception difficult to detect by US)
 
-Blood cx
 
-ESR
 
-consider CT abdomen (ileoileal intussusception difficult to detect by US)
 


==DDx==
==DDx==
 
#meningococcemia (febrile, ill appearing)
 
#erythema nodosum
-meningococcemia (febrile, ill appearing)
 
-erythema nodosum
 


==Treatment==
==Treatment==
 
*dz self limited: 94% recover completely
 
*consider corticosteroids for severe disease (abdominal pain, hematuria, arthralgias)
-dz self limited: 94% recover completely
**prednisone 1mg/kg/day
 
-consider corticosteroids for severe disease (abdominal pain, hematuria, arthralgias)
 
    -prednisone 1mg/kg/day
 


==Disposition==
==Disposition==
 
*most patients managed safely as outpatient
 
*consider admission for:
-most patients managed safely as outpatient
**uncertain diagnosis to exclude possibility of meningococcemia
 
**severe abdominal pain and vomiting
-consider admission for:
 
    -uncertain diagnosis to exclude possibility of meningococcemia
 
    -severe abdominal pain and vomiting
 
 


==Source==
==Source==
Adapted from Rosens 7th edition
Adapted from Rosens 7th edition


[[Category:Peds]]
[[Category:Peds]]

Revisión del 19:32 7 jun 2011

Background

-HSP, aka anaphylactoid purpura

-systemic vasculitis associated with abdominal pain and rash

-usually age 4-11, may occur in adults

-commonly occurs in springtime after viral URI

Diagnosis

-clinical diagnosis based on presence of abdominal pain, classic rash, microscopic hematuria, arthralgias in otherwise well appearing child

-symptoms: abdominal pain, nausea, vomiting, diarrhea, rash, mild arthralgias

-rash: palpable purpura on buttocks and lower extremities

-intussusception: ileoileal more common than ileocolic inpatients with HSP

Work-Up

  1. CBC, Chem7
  2. UA
  3. Blood cx
  4. ESR
  5. consider CT abdomen (ileoileal intussusception difficult to detect by US)

DDx

  1. meningococcemia (febrile, ill appearing)
  2. erythema nodosum

Treatment

  • dz self limited: 94% recover completely
  • consider corticosteroids for severe disease (abdominal pain, hematuria, arthralgias)
    • prednisone 1mg/kg/day

Disposition

  • most patients managed safely as outpatient
  • consider admission for:
    • uncertain diagnosis to exclude possibility of meningococcemia
    • severe abdominal pain and vomiting

Source

Adapted from Rosens 7th edition