Diferencia entre revisiones de «Budd-Chiari syndrome»
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==Background== | ==Background== | ||
*Rare | *Rare | ||
*Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass) | |||
*Fulminant, acute, chronic, or asymptomatic. | *Fulminant, acute, chronic, or asymptomatic. | ||
==Clinical Features== | ==Clinical Features== | ||
* Classic triad: abdominal pain, [[ascites]], and [[hepatomegaly]] | * Classic triad: [[abdominal pain]], [[ascites]], and [[hepatomegaly]] | ||
==Differential Diagnosis== | ==Differential Diagnosis== | ||
*[[Hepatitis]] | *[[Hepatitis]] | ||
*[[Cirrhosis]] | *[[Cirrhosis]] | ||
==Evaluation== | ==Evaluation== | ||
*LFTs, | *[[LFTs]], BMP, LDH | ||
* Ultrasound, retrograde angiography | * Ultrasound, retrograde angiography | ||
*CT and MRI less sensitive | *CT and MRI less sensitive | ||
==Management== | ==Management== | ||
* | *Sodium restriction, [[diuretics]], [[anticoagulants]] | ||
*venous shunts or TIPS | *venous shunts or TIPS | ||
*liver transplant | *liver transplant | ||
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<references/> | <references/> | ||
[[Category: | [[Category:GI]] | ||
Revisión del 17:48 27 mar 2017
Background
- Rare
- Caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
- Fulminant, acute, chronic, or asymptomatic.
Clinical Features
- Classic triad: abdominal pain, ascites, and hepatomegaly
Differential Diagnosis
Evaluation
- LFTs, BMP, LDH
- Ultrasound, retrograde angiography
- CT and MRI less sensitive
Management
- Sodium restriction, diuretics, anticoagulants
- venous shunts or TIPS
- liver transplant
