Diferencia entre revisiones de «Restrictive cardiomyopathy»
(Text replacement - "==Diagnosis==" to "==Evaluation==") |
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| Línea 16: | Línea 16: | ||
**Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity) | **Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity) | ||
**Radiation, chemotherapy (doxorubicin) | **Radiation, chemotherapy (doxorubicin) | ||
**Metastatic disease, carcinoid syndrome | **Metastatic disease, [[carcinoid syndrome]] | ||
==Evaluation== | ==Evaluation== | ||
Revisión del 15:53 7 sep 2016
Background
- Muscle is stiff from fibrosis or infiltrating process
- EF is usually normal
- Form of diastolic dysfunction (difficulty filling)
- Must distinguish from constrictive pericarditis
Differential Diagnosis
Cardiomyopathy
- Dilated cardiomyopathy
- Hypertrophic cardiomyopathy
- Restrictive cardiomyopathy
- Peripartum cardiomyopathy
- Takotsubo cardiomyopathy
- Arrhythmogenic right ventricular dysplasia
- Restrictive cardiomyopathy ddx
- Idiopathic
- Familial noninfiltrative disease
- Infiltrative disease (amyloidosis, sarcoidosis, Gaucher, Hurler)
- Storage diseases (hemachromatosis, Fabry, glycogen/lysosomal storage diseases)
- Diabetes
- Scleroderma
- Endomyocardial fibrosis (hypereosinophilic syndrome, medication toxicity)
- Radiation, chemotherapy (doxorubicin)
- Metastatic disease, carcinoid syndrome
Evaluation
- Consider if CHF but no evidence of cardiomegaly or systolic dysfunction
Management
- Symptom directed (diuretics and ACEI)