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==Background==
==Background==
-HSP, aka anaphylactoid purpura
*Usually affects 2-11yr
 
*5% of cases are a/w intussusception (abd vasculitis)
-systemic vasculitis associated with abdominal pain and rash
*Renal involvement is feared complication
 
*95% recover completely
-usually age 4-11, may occur in adults
 
-commonly occurs in springtime after viral URI


==Diagnosis==
==Diagnosis==
-clinical diagnosis based on presence of abdominal pain, classic rash, microscopic hematuria, arthralgias in otherwise well appearing child
*Triad:
**Purpuric rash (lower extremity, buttock)
**Acute abdominal pain (Diffuse, colicky)
***Develops after onset of rash
**Arthritis
***Migratory, usually involves knees/ankles


-symptoms: abdominal pain, nausea, vomiting, diarrhea, rash, mild arthralgias
==DDx==
 
#Meningococcemia
-rash: palpable purpura on buttocks and lower extremities
#Erythema nodosum
 
#Intussusception
-intussusception: ileoileal more common than ileocolic inpatients with HSP
#Rheumatic fever
#Polyarteritis nodosa
#SLE
#RA
#Drug reaction


==Work-Up==
==Work-Up==
#CBC, Chem7
#UA
#UA
#Blood cx
##If +hematuria obtain chemistry
#ESR
#consider CT abdomen (ileoileal intussusception difficult to detect by US)
 
==DDx==
#meningococcemia (febrile, ill appearing)
#erythema nodosum


==Treatment==
==Treatment==
*dz self limited: 94% recover completely
*Supportive
*consider corticosteroids for severe disease (abdominal pain, hematuria, arthralgias)
*NSAIDs for pain
**prednisone 1mg/kg/day


==Disposition==
==Disposition==
*most patients managed safely as outpatient
*Outpt management for most w/ rheum f/u
*consider admission for:
**uncertain diagnosis to exclude possibility of meningococcemia
**severe abdominal pain and vomiting


==Source==
==Source==
Adapted from Rosens 7th edition
Rosen's, Tintinalli


[[Category:Peds]]
[[Category:Peds]]

Revisión del 23:37 22 jun 2011

Background

  • Usually affects 2-11yr
  • 5% of cases are a/w intussusception (abd vasculitis)
  • Renal involvement is feared complication
  • 95% recover completely

Diagnosis

  • Triad:
    • Purpuric rash (lower extremity, buttock)
    • Acute abdominal pain (Diffuse, colicky)
      • Develops after onset of rash
    • Arthritis
      • Migratory, usually involves knees/ankles

DDx

  1. Meningococcemia
  2. Erythema nodosum
  3. Intussusception
  4. Rheumatic fever
  5. Polyarteritis nodosa
  6. SLE
  7. RA
  8. Drug reaction

Work-Up

  1. UA
    1. If +hematuria obtain chemistry

Treatment

  • Supportive
  • NSAIDs for pain

Disposition

  • Outpt management for most w/ rheum f/u

Source

Rosen's, Tintinalli