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| ==Background==
| | #REDIRECT[[Porphyria]] |
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| ==Clinical Features==
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| ==Differential Diagnosis==
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| ==Diagnosis==
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| ==Management==
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| *Analgesia
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| *Glucose load
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| **Decreases porphyrin production
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| **Typical protocol is D10W 3-4 liters daily x 4 days
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| **Risk of hyponatremia given significant free water load
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| *Hemin
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| **Decreases porphyrin production, significantly more potent than glucose
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| **Recommended for most cases requiring hospitalization, or any with neurologic symptoms
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| **3-4 mg/kg daily for 4 days
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| **Can cause significant infusion site phlebitis - minimize by reconstituting in 25% albumin; consider central venous administration
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| **Very expensive - around $8000 per 313 mg vial
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| ==Disposition==
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| ==See Also==
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| ==External Links==
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| http://www.porphyriafoundation.com/
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| ==References==
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| <references/>
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