Diferencia entre revisiones de «Budd-Chiari syndrome»
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[[Category:Neuro]] | |||
Revisión del 06:02 27 mar 2017
Background
- Rare; caused by occlusion of hepatic veins, 75% primary (thrombosis), 25% secondary (compression by mass)
- Fulminant, acute, chronic, or asymptomatic.
Clinical Features
- Classic triad: abdominal pain, ascites, and hepatomegaly
Differential Diagnosis
Evaluation
- LFTs, creatinine, urea, electrolytes, LDH
- Ultrasound, retrograde angiography
- CT and MRI less sensitive
Management
- sodium restriction, diuretics, anticoagulants
- venous shunts or TIPS
- liver transplant
